WHAT IS MACULAR AMYLOIDOSIS?Macular amyloidosis is a rare skin condition that causes brown patches to develop in a characteristic wavy or ridged pattern. It may also be itchy. It often appears on the upper back or shoulders, chest, or arms and legs. It is most common in people with darker skin tones; often originally from Asia, South America, or the Middle East.
![Amyloidosis cutis maculosa (click on photo to enlarge) [source: www.skin-diseases.eu] Amyloidosis cutis maculosa](../../images/maculaire-amyloidosis-1z.jpg) |
![Amyloidosis cutis maculosa (click on photo to enlarge) [source: www.skin-diseases.eu] Amyloidosis cutis maculosa](../../images/maculaire-amyloidosis-2z.jpg) |
![Amyloidosis cutis maculosa (click on photo to enlarge) [source: www.skin-diseases.eu] Amyloidosis cutis maculosa](../../images/maculaire-amyloidosis-3z.jpg) |
| macular amyloidosis |
macular amyloidosis |
macular amyloidosis |
![Amyloidosis cutis maculosa (click on photo to enlarge) [source: www.skin-diseases.eu] Amyloidosis cutis maculosa](../../images/maculaire-amyloidosis-4z.jpg) |
![Amyloidosis cutis maculosa (click on photo to enlarge) [source: www.skin-diseases.eu] Amyloidosis cutis maculosa](../../images/maculaire-amyloidosis-5z.jpg) |
![Amyloidosis cutis maculosa (click on photo to enlarge) [source: www.skin-diseases.eu] Amyloidosis cutis maculosa](../../images/maculaire-amyloidosis-6z.jpg) |
| macular amyloidosis |
macular amyloidosis |
wave pattern |
HOW DOES MACULAR AMYLOIDOSIS DEVELOP?The exact cause is unknown. It is known that a specific protein called amyloid is stored in the skin. This protein comes from damaged skin cells. But why this happens is unknown. Itching and scratching may play a role. There may also be a genetic predisposition, as it occurs in certain population groups and can run in families. There are no known underlying diseases.HOW IS THE DIAGNOSIS MADE?The diagnosis is usually made based on the clinical picture, i.e., its appearance. The diagnosis can be confirmed by taking a skin biopsy. Special stains can reveal the presence of amyloid protein.HOW IS MACULAR AMYLOIDOSIS TREATED?Macular amyloidosis is difficult to treat. It's recommended to use nourishing creams or lotions that prevent the skin from drying out and itching. Sometimes mild anti-inflammatory creams (corticosteroids) or anti-itch medications are prescribed. However, these don't make the spots go away. It's important to try not to scratch them, as this can worsen the condition.WHAT ARE THE OUTLOOK?Macular amyoidosis usually doesn't go away on its own; it can spread slowly. It's not a dangerous skin condition, but it can be bothersome due to the itching and skin discoloration. |